________________________________________________________
IV Meeting
on the
MOLECULAR
MECHANISMS OF NEURODEGENERATION
Aula Magna, Universita' degli Studi di Milano
Via Festa del Perdono 7 - 20122 Milano (Italy)
May 8-10, 2009
FINAL PROGRAM
Friday, May 08, 2009 (Morning)
09:30 Registration
10:00 Satellite
symposium on:
Molecular
Mechanisms on Neurodevelopment
Axonal
development and targeting
(no
registration required for this symposium)
Chairpersons: Roberto Maggi (Italy), Ivan De
Curtis (Italy)
10:15-11:00 Patricia
Salinas (UK)
"Wnt signaling in the regulation of synapse formation and maintenance"
11:00-11:30 Ivan
De Curtis (Italy)
"Essential
role of Rac GTPases in neuronal development"
11:30-12:00 Flavia
Valtorta (Italy)
"Membrane
trafficking in axonal growth cones"
12:00-12:30 Giorgio
Merlo (Italy)
"Transcription
factor regulations of axon targeting: the olfactory system"
Closing remarks
Friday,
May 08, 2009 (Afternoon)
Opening
Session
14:00 Introduction
by the organizers
Angelo Poletti, Elena Cattaneo, Franco
Taroni (Italy)
14:10-14:30 Gianpiero
Sironi (Prorettore alla ricerca, Universita' di Milano)
Stefano Di Donato (Direttore
Scientifico Emerito,
Fondazione Istituto
Neurologico "Carlo Besta" Milano)
Opening
lecture
14:30-15:30 Aaron
Ciechanover (Israel)
The Nobel Prize in Chemistry 2004
"The
Ubiquitin Proteolytic System: From
Basic Mechanisms via Human Diseases and onto Drug Targeting"
Introduced
by Ron R. Kopito (USA)
Session I:
Cellular handling of aberrant neurotoxic proteins I
Chairpersons:
Marcy McDonald (USA), Caterina Bendotti (Italy)
15:30-16:00 Ron
Kopito (USA)
"Membrane
penetration and prion-like propagation of amyloids"
16:00-16:30 Ana
Maria Cuervo (USA)
"Degradation
of misfolded proteins through the autophagic system in the central nervous
system"
16:30-17:00 Francesco
Fornai (Italy)
"The
role of autophagy in selective neuronal degeneration: basic evidence and
pharmacological manipulation"
17:00-17:30 Coffee
break
Session
II: Cellular handling of aberrant neurotoxic proteins II
Chairpersons:
Piera Pasinelli, (USA), Mario Salmona (Italy)
17:30-18:00 Christopher E. Shaw (UK)
"TDP-43
mutations in familial and Sporadic Amyotrophic Lateral Sclerosis "
18:00-18. 30 J.
Paul Taylor (USA)
"Insights into the pathogenesis of
TDP-43-related disease from Drosophila models"
18:30-19:00 Erich
E. Wanker (Germany)
"Modulation
of amyloid formation pathways with chemical chaperones"
19:00-19:30 Gianluigi
Forloni (Italy)
"Protein toxicity in AD and PD "
19:30 Welcome
Party
Saturday, May 9, 2009 (Morning)
Session III: Mitochondria, oxidative stress, and genotoxicity I
Chairpersons:
Silvia De Biasi (Italy), Massimo Stefani (Italy)
09:00-09:30 Eva-Maria Mandelkow (Germany)
"Modes of TAU toxicity and neuronal degeneration"
09:30-10:00 Paolo
Bernardi (Italy)
"Toward a Mitochondrial Therapy of Collagen VI Muscular Dystrophies.""
10:00-10:30
Franco Taroni (Italy)
"Mitochondrial maintenance and
spinocerebellar degeneration"
10:30-11:00 coffee
break
Session IV: Mitochondria, oxidative stress, and genotoxicity II
Chairpersons:
Armando Gennazzani (Italy), Davide Trotti (USA)
11:00-11:30 Robert H.
Brown (USA)
"Genetic
determinants of Amyotrophic Lateral Sclerosis"
11:30-12:00 Vittorio
Calabrese (Italy)
"Nitric
Oxide in the brain: neuroprotection versus neurotoxicity"
12:00-12:30 Keith W.
Caldecott (UK)
"Chromosomal
Single-strand break repair and neurological disease"
12:30-13:30 Lunch
Saturday,
May 9, 2009 (Afternoon)
13:30-15:00
Poster Session I (P01-P66)
Session V:
Role of microRNAs in the neuronal functions and dysfunctions
Chairpersons:
Robert M. Friedlander (USA), Robert G. Korneluk (Canada)
15:00-15:30 Asa
Abeliovich (USA)
"A
MicroRNA feedback circuit in midbrain dopamine neurons"
15:30-16:00 Carlo Cogoni
(Italy)
"MicroRNA in the brain"
16:00-17:00
Selected
Free Communication
Chairpersons:
Franco Taroni (Italy), Giorgio Casari (Italy)
OC1 - Role of miRNAs regulation on CDK5R1 expression in
Alzheimer's disease
Moncini
S, Zuccotti P, Venturin M, Salvi A, Sabelli C, De Petro G, Barlati S, Riva
P. (Italy)
OC2 - Identifying genes that modify Huntington's disease in the
N171-82Q mouse model.
Corrochano-Sanchez S, Acevedo-Arozena
A, Rubinsztein DC, Brown SDM (UK)
OC3 - Modifiers of aggregation in neurodegenerative diseases
Holmberg M, van Ham TJ, Thijssen KL,
van Rheenen J, van Veluw J, Hofstra RMW, Nollen EAA (The Netherland)
OC4 - Analysis of inducible mouse model of Huntington disease
combined with ubiquitin-proteasome system reporter mice.
Ortega
Z, Maynard CJ, Diaz-Hernandez
M, Dantuma NP, Lucas JJ (Spain)
17:00-17:30 Coffee
break
17:30-19:30
Selected
Free Communication
Chairpersons:
Franco Taroni (Italy), Giorgio Casari (Italy)
OC5 - Polyglutamine toxicity induces multiple photoreceptor
degeneration pathways and complex retinal remodelling in a SCA7 mouse model
Trottier
Y, Messaddeq N, Jacquard C, Weber C, Karem A, Wolfrum U, Jonet L, Jeanny
JC, Yefimova MG (France)
OC6 - AGLF2 mutations cause autosomal dominant ataxia and
DiBella D, Lazzaro F, Brusco A,
Battaglia G, Pastore A, Finardi A, Fracasso V, Magri S, Plumari M, Cagnoli C,
Tempia F, Brussino A, Gellera C, Mariotti C, Plevani P, DiDonato S, Langer T,
Muzi-Falconi M, Taroni F (Italy)
OC7 - Heat shock response and misfolded protein elimination
associated with PHOX2B polyalanine expansion and GFAP mutations in congenital
central hypoventilation syndrome and Alexander disease
Bachetti T, Di Zanni E, Bocca P,
Borghini S, Prigione I, Caroli F, Filocamo M, Balbi P, Biancheri R, Ravazzolo
R, Ceccherini I (Italy)
OC8 - Molecular mechanism of the regulation of two ER
stress-mediated degradation system, UPS and autophagy/lysosome, of the
misfolded protein.
Kouroku
Y, Fujita E, Momo YM, Momoi T (Japan)
OC9 - Polyglutamine atrophin provokes autophagic
neurodegeneration by repressing the tumour suppressor FAT
Charroux
B, Occhi S, Nisoli I, Napoletano F, Chauvin JP, Calamita P, Volpi VG, Zanin
V, Fanto M (Italy)
OC10 - The nucleolus as source of oxidative damage and
neurodegeneration.
Parlato
R, Rieker C, Kreiner, Engblom D, Bierhoff H, Grummt I, Schutz G (Germany)
OC11 - Aggresome-forming TTRAP mediates pro-apoptotic properties
of ParkinsonŐs disease-associated DJ-1 missense mutations
Zucchelli S, Vilotti S, Calligaris R,
Lavina ZS, Biagioli M, Foti R, De Maso L, Pinto M, Gorza M, Speretta E,
Casseler C, Tell G, Del Sal G, Gustincich S (Italy)
OC12 - Role of dopamine-induced calcium signalling in
neurodegeneration of control and PINK1 knockout neurons and astrocytes.
Vaarmann A, Abramov AY (UK)
20:30 Social
Dinner
Sunday,
May 10, 2009 (morning)
08:30-10.00 Selected
Free Communications
Chairpersons:
Angelo Poletti (Italy), Giorgio Battaglia (Italy)
OC13 - Role of PPP4R2 in apoptosis and neuritogenesis
Bosio Y, Camera P, Berto G, Ambrogio
C, Silengo L, Di Cunto F (Italy)
OC14
- The Zing Finger
protein ZPR1 deficiency causes activation of the JNK signaling cascade and
neuron degeneration
Ahmad S, Gangwani L (USA)
OC15 - Influence of post-translational modifications on the
androgen receptor in SBMA
Jochum T, Ritz ME, Moss D, Cato ACB
(Germany)
OC16
- Effect of selective
androgen receptor modulators in SBMA experimental models.
Bolzoni E, Orr CR, Liu Y, McDonnell D, Wilson E, Merry DE (USA).
OC17 - Disruption of dynein/dynactin function in neurons in vivo
does not lead to motor abnormalities in transgenic mice and improves lifespan
in the SOD1-ALS mouse model
Teuling E, van Dis V, Wulf PS,
Haasdijk ED, Akhmanova A, Hoogenraad CC, Jaarsma D (USA)
OC18
- Spinal cord from an
animal model of ALS: a potential source of adult neural stem cells in response
to neurodegeneration.
Marcuzzo S, Preite L, Cappelletti C, Zingale
A, Terragni B, Mantegazza M,
Bernasconi P, Mantegazza R (Italy)
10:00-10:30 coffee
break
Session VI: Altered protein
functions in neurodegenerative diseases
Chairpersons:
Marian Di Figlia (USA), Neil Aronin (USA)
10:30-11:00 Angelo
Poletti (Italy)
"Clearance of misfolded proteins in SBMA and ALS"
11:00-11:30
Daniela Rossi (Italy)
"Role
of astroglia on motor neuron cell survival and death in ALS"
11:30-12:00
Elena Cattaneo (Italy)
"BDNF,
Huntingtin and neuronal cell death"
12:00-12:30 Patrik
Brundin (Sweden)
"Can
Parkinson's Disease pathology be propagated from one neuron to another?"
12:30-13:30 Lunch
Sunday,
May 10, 2009 (afternoon)
13:30-15:00 Poster
Session II (67-133)
Session
VI: Genetic determinants of Neurodegenerative diseases
Chairpersons:
Elena Cattaneo
(Italy), Stefano DiDonato (Italy)
15:00-15:30 Fabrizio Tagliavini (Italy)
"Good Gene, Bad Gene:
New APP Variant May Be Both"
15:30-16:00
Piera Pasinelli (USA)
"Alteration
of mitochondrial functions in amyotrophic lateral sclerosis"
16:00-16:30 James F. Gusella (USA)
"Modifier
genes in Huntington's disease"
16:30-17:00 Michael
R. Hayden (Canada)
"Bad
Boys and the Pathogenesis of HD"
17:00 Closing
Remarks
POSTERS
Poster
Session I (P01-P66)
Saturday,
May 9, 2009
from 13:30
to 15:00
________________________________________________________________________
P01 - ALS
GENES: MUTATIONAL ANALYSIS IN A LARGE COHORT OF ITALIAN PATIENTS
Gellera
C*, Ticozzi N, Ratti A, Corrado L, Castellotti B, Colombrita C, Plumari M,
Carlomagno Y, Bragato C, Mazzini L, Taroni F, Silani V
P02 - DOWN CRITICAL REGION-ENCODED
PROTEIN TTC3 INHIBITS NEURONAL DIFFERENTIATION IN HIPPOCAMPAL NEURONS
Berto
G*, Camera P, Dotti CS, Di Cunto F
P03 - AN OLD PROTEIN IN
UNEXPECTED PLACES: ALPHA- AND BETA- GLOBIN EXPRESSION IN MESENCEPHALIC
DOPAMINERGIC NEURONS AND GLIAL CELLS
Biagioli
M*, Pinto M*, Cesselli D, Zaninello M, Lazarevic D, Simone R, Vlachouli C,
Plessy C, Bertin N, Beltrami A, Kobayashi K, Gallo V, Santoro C, Ferrer I,
Rivella S, Beltrami CA, Carninci P, Raviola E, Gustincich S
P04 - MUTATIONAL SCREENING AND
FUNCTIONAL ANALYSES IN THE ZEBRAFISH MODEL OF GIGYF2 AS A CANDIDATE GENE FOR
PARKINSON DISEASE
Guella
I*, Del Giacco L, Asselta R, Pistocchi A, Rimoldi V, Sironi F, Primignani P,
Zini M, Pezzoli G, Duga S, Goldwurm S
P05 - FMR1 GENE
TESTING IN THE FAMILY WITH ATAXIA AND TREMOR
Rajkiewicz
M, Kaca-Orynska M, Sulek-Piatkowska A, Krysa W, Koziorowski D, Friedman A
P06 - MODELING THE NEUROLOGICAL
FEATURES OF TUBEROUS SCLEROSIS COMPLEX BY SELECTIVE TARGETING OF EMBRYONIC AND
ADULT NEURAL STEM CELLS IN MICE
Magri
L, Galli R
P07 - RELATIONSHIP BETWEEN AF4
EXPRESSION LEVELS AND THE TIME FRAME/ONSET OF NEURODEGENERATION IN THE ROBOTIC
MOUSE
Mattia
J Finelli*, Emmanuelle Bitoun, Sheena Lee, Peter L Oliver, Kay E Davies
P08 - A MODEL OF SPINOCEREBELLAR
ATAXIA TYPE 2 (SCA2): THE (CAG)102-SCA2 KNOCK-IN MOUSE
Damrath
E*, Gispert S, Nonis FD, Lastres-Becker I, Nowock J, Auburger G
P09 - MUTATION ANALYSIS OF THE
SPG11 AND SPG15 GENE IN ITALIAN PATIENTS WITH SPASTIC PARAPLEGIA AND THIN
CORPUS CALLOSUM
Castellotti
B*, Mariotti C, Pensato V, Fancellu R, Salsano E, Gellera C, Pareyson D, Taroni
F
P10 - ALPHA-SYNUCLEIN POINT
MUTATION ANALYSIS IN ITALIAN PATIENTS WITH AUTOSOMAL DOMINANT PARKINSON DISEASE
Francesca
Sironi, Luca Trotta, Michela Zini, Silvana Tesei, Paola Primignani, Tiziana
Brambilla, Domenico A Coviello, MD, Gianni Pezzoli, MD, Stefano Goldwurm
P11 -
ALTERNATIVE SPLICING ENHANCES LYSINE SPECIFIC DEMETHYLASE 1 (LSD1) EPIGENETIC TUNEABILITY IN THE MAMMALIAN NERVOUS SYSTEM.
Zibetti C*, Mattevi A, Sala C, Battaglioli E
P12 - INCREASED SUSCEPTIBILITY
OF CORTICAL SPREADING DEPRESSION IN ATP1A2 KNOCK-IN MOUSE MODEL OF FAMILIAL
HEMIPLEGIC MIGRAINE TYPE2
Loredana
Leo, Lisa Gherardini, Virginia Barone, Tommaso Pizzorusso, Giorgio Casari
P13 - HAPLOINSUFFICIENCY OF
AFG3L2, THE GENE RESPONSIBLE FOR SPINOCEREBELLAR ATAXIA TYPE 28 (SCA28), CAUSES
MITOCHONDRIAL-MEDIATED PURKINJE CELL DEGENERATION
Maltecca
F*, Magnoni R, Cox G, Quattrini A, Casari G
P14 - ROLES OF ERYTHROPOIETIN
AND SONIC HEDGEHOG IN NEUROPROTECTIVE EFFECTS OF BRAIN-DERIVED NEUROTROPHIC
FACTOR AGAINST MITOCHONDRIAL DYSFUNCTION
Ding-I
Yang*, Chia-Lin Wu
P15 - INTERPLAY BETWEEN
GLUTAMINE AVAILABILITY, GLUTAMATE AND GLUTATHIONE IN A CELL MODEL FOR FAMILIAL
FORMS OF AMYOTROPHIC LATERAL SCLEROSIS
DŐAlessandro
G*, Calcagno E, Tartari S, Rizzardini M, Invernizzi RW, Cantoni L
P16 - NEURAL TUBE DEFECTS
Angeles
Cavero
P17 - NITROPROTEOMICS OF
PERIPHERAL BLOOD MONONUCLEAR CELLS FROM PATIENTS AND RAT MODEL OF ALS
Pozzi
S*, Nardo G, Lauranzano E, Mantovani S, Garbelli S, Marinou K, Basso M, Mora G,
Bendotti C, Bonetto V
P18 - TOWARDS THE BIOCHEMICAL
CHARACTERIZATION OF SELADIN-1/DHCR24: HETEROLOGOUS PRODUCTION OF THE HUMAN
PROTEIN
Zucchini
D, Caprini G, Criaco L, Vanoni MA
P19 - MORPHOLOGICAL CHANGES IN
HUNTINGTON'S DISEASE MITOCHONDRIA SUSTAIN THEIR INCREASED SUSCEPTIBILITY TO
APOPTOTIC STIMULI
Veronica
Costa*, Dmitry Lim, Ernesto Carafoli, Mauro Piacentini, Walter Malorni, Luca
Scorrano
P20 - STUDIES ON CONE CELL DEATH
MECHANISMS IN THE CPFL1 MOUSE MODEL
Trifunovic
D*, Dengler K, Michalakis S, Biel M, Paquet-Durand F
P21 - APOPTOSIS INDUCED BY
PLATINUM COMPOUNDS IN B50 CELLS
Santin
G*, Bottone MG, Piccolini VM, Veneroni P, De Pascali SA, Migoni D, Marsigliante
S, Fanizzi FP, Bernocchi G
P22 - CISPLATIN ANALOGUES WITH
NEW SUBCELLULAR TARGETS: A STRATEGY TO PREVENT NEUROTOXICITY INDUCED BY
PLATINUM COMPOUNDS?
Cerri
S*, De Pascali SA, Migoni D, Marsigliante S, Fanizzi FP, Bernocchi G
P23 - IN VIVO CHARACTERIZATION
OF HUMAN NEURAL STEM ECLLS IMMORTALIZED WITH v-MYC (IhNSC) BY TRANSPLANTATION
INTO ISCHEMIC RAT BRAIN
Lidia
De Filippis, Laura Rota Nodari, Daniela Ferrari, Fabrizio Giani, Cristina
Zalfa, Guido Santilli, Angelo Luigi Vescovi
P24 - ABETA AGGREGATE TOXICITY
DEPENDS ON MEMBRANE CHOLESTEROL CONTENT IN FAMILIAL ALZHEIMER'S FIBROBLASTS
Evangelisti
E*, Zampagni M, Wright D, Liguri G, Puccetti B, Bagnoli S, Nacmias B, Sorbi S,
Cecchi C
P25 - INVOLVMENT OF D-SERINE
RACEMASE DURING NEURONAL CELL DEATH
Nadia
Canu, Fulvio Florenzano, Anna di Luzio, Tiziana Borsello, Maria Teresa Ciotti
P26 - MITOCHONDRIAL INVOLVEMENT
IN CLN1 FIBROBLASTS
Pezzini
F*, Sembenini D, Vattemi G, Tonin P, Gismondi F, Marconi MG Carrozzo R,
Santorelli FM, Simonati A
P27 - PINK1 AND MITOCHONDRIAL
DYSFUNCTION IN NEURONS AND SKELETAL MUSCLE CELLS
Zhi
Yao, Sonia Gandhi, Iain Hargreaves, Helene Plun-Favreau, Andrey Y Abramov, Nicholas
W Wood
P28 - CERULOPLASMIN DIFFERENTIAL
EXPRESSION IN THE CEREBROSPINAL FLUID OF PARKINSON'S DISEASE REFLECTS OXIDATION
AND FUNCTIONAL IMPAIRMENT FAVOURING INTRACELLULAR IRON OVERLOAD
Olivieri
S, Iannaccone S, Conti A, Cannistraci CV, Piccio L, Franciotta D, Cappa S,
Alessio M
P29 - ANALYSIS OF IRON
HOMEOSTASIS IN SKIN FIBROBLASTS FROM PANTOTHENATE KINASE ASSOCIATED
NEURODEGENERATION PATIENTS
Campanella
A, Rovelli E, Garavaglia B, Levi S
P30 - BETA-AMYLOID ACTIVATES
PARP THROUGH FREE RADICAL GENERATION BY THE NADPH OXIDASE
Abeti
R*, Abramov AY, Duchen MR
P31 - GENOPOLIS CONSORTIUM FOR
FUNCTIONAL GENOMICS- THE CORE FOR EXPLOITING MICROARRAY THECNOLOGIES
Biancolini
D, Papagna A, Lenzken C, Bonanno D, Barabino SML, Castagnoli-Ricciardi P,
Calogero RA, Zolezzi F*
P32 - MITOCHONDRIAL DYSFUNCTION
IN EXPERIMENTAL CHARCOT-MARIE-TOOTH TYPE 1A (CMT1A) NEUROPATHY
Lucilla
Nobbio*, Fulvia Fiorese Valeria Prada, Silvia Ravera, Mariapaola Nitti, Angelo
Schenone
P33 - AXONUCLEAR COMMUNICATION
SYSTEM IS ALTERED IN MOTOR NEURONS OF RODENT MODELS OF FAMILIAL AMYOTROPHIC
LATERAL SCLEROSIS
Peviani
M*, Spano G, Pagani A, Bendotti C
P34 - PURKINJE CELL AXONAL
INJURY IN THE CEREBELLUM OF Ts65Dn MICE: ROLE OF BETA-AMYLOID OVERLOAD
Lomoio
S*, Necchi D, Scherini E
P35 - PENTAPEPTIDES DERIVED FROM
A-BETA 1-42 PROTECT NEURONS FROM THE MODULATORY EFFECT OF A-BETA OLIGOMER IN
VIVO ELECTROPHYSIOLOGICAL STUDIES
Chiovini
B*, Barkczi B, Juhsz G, FÄlp L, Penke B, Szegedi V
P36 - SYNAPTIC PLASTICITY
STUDIES IN APOB-100 TRANSGENIC MICE IN CORRELATE TO ALZHEIMERŐS DISEASE
Chiovini
B*, Barkczi B*, Juhsz G, Bereczki E, Sntha M, Penke B, Szegedi V
P37 - MUTANT PRION PROTEIN
EXPRESSION IS ASSOCIATED TO AN ALTERATION OF THE RAB GDP DISSOCIATION INHIBITOR
ALPHA(GDI)/RAB11 PATHWAY
Massignan
T, Biasini E, Salmona M, Harris DA, Chiesa R, and Bonetto V
P38 - CHARACTERIZATION OF
DETERGENT-INSOLUBLE PROTEINS IN ALS MODELS AND PATIENTS INDICATES A POSSIBLE
CAUSAL LINK BETWEEN NITRATIVE STRESS AND AGGREGATION IN PATHOGENESIS
Manuela
Basso, Giuseppina Samengo, Giovanni Nardo, Tania Massignan, Giuseppina
DŐAlessandro, Silvia Tartari, Lavinia Cantoni, Marianna Marino, Cristina
Cheroni, Silvia De Biasi, Mario Salmona, Caterina Bendotti, Valentina Bonetto*
P39 - THE ACTIVITY OF NMDA
RECEPTOR IS ENHANCED BY THE FIBRILLAR A-BETA 1-42 VIA THE INTEGRIN RECEPTOR
PATHWAY
Barkczi
B*, Chiovini B, Juhsz G, FÄlp L, Penke B, Szegedi V
P40 - ALPHA-SYNUCLEIN IS AN
ACTIN BINDING PROTEIN AND ITS A30P MUTANT AFFECTS THE CYTOSKELETON STRUCTURE
AND DYNAMICS
Bellani
S*, Sousa VL, Giannandrea M, Meldolesi J, Valtorta F, Chieregatti E
P41 - ACUTE OR CHRONIC
CO-TREATMENT WITH 1-METHYL-4-PHENYLPYRIDINIUM (MPP+) AND EPOXOMICIN IN
ORGANOTYPIC CULTURES OF MOUSE MESENCEPHALON: SYNERGISTIC TOXICITY OR
ALPHA-SYNUCLEIN AGGREGATES?
Rossen
S, Larsen TR, Gramsbergen JB
P42 - MIS-SPLICING OF
MICROTUBULE-ASSOCIATED TAU IN MYOTONIC DYSTROPHY TYPE: IMPLICATION OF CUGBP1
AND MBNL1
Dhaenens
CM, Tran H, Schraen-Maschke, Sistiaga, A, Goicoechea M, Obriot H, Ghanem D, Van
Brussel E, Gavaert MH, Maurage CA, Buae L, Sablonniare B, Lopez de Munain A,
Caillet-Boudin ML, Sergeant N
P43 - ATAXIN-3 BINDS TUBULIN
WITH HIGH AFFINITY
Mazzucchelli
S*, De Palma A, DŐurzo A, Pozzi C, Pastori V, Comelli F, Fusi P, Vanoni M,
Tortora P, Mauri PL, Regonesi ME
P44 - EXPERIMENTAL MODELS:
TOWARD STUDYING MECHANISMS OF NEUROFIBRILLARY DEGENERATION
Hamdane
M*, Desmerciares J, Burnouf S, Bouafia H, Belarbi K, Troquier L, Demeyer D,
Grosjean ME, Caillierez R, Barbot B, Brion I, Fernandez Gomez FJ, Humez S,
Sergeant N, Blum D, Buae L
P45 - INHIBITION OF CALPAINS
PREVENTS TRANSLOCATION OF MUTANT ATAXIN-3 TO THE NUCLEUS AND REDUCES
NEURODEGENERATION IN A LENTIVIRAL MOUSE MODEL OF MACHADO-JOSEPH DISEASE
Simoes
AT*, Goncalves N, Nbrega C, Deglon N, Bandeira Duarte C, Kugler S, Pereira de
Almeida L
P46 - ADENOSINE A2A RECEPTORS
ANTAGONISM DELAYS NEURODEGENERATION IN A LENTIVIRAL MOUSE MODEL OF MACHADO
JOSEPH DISEASE
Goncalves
N*, Simoes AT Cunha R, Pereira de Almeida L
P47 - COMPARATIVE ANALYSIS OF
STRUCTURAL AND FUNCTIONAL PROPERTIES OF BETA-AMYLOID AGGREGATED SPECIES
Denise
Ferrera*, Claudio Canale, Fabio Benfenati, Laura Gasparini
P48 - SIMILAR OLIGOMERS OF
HYPF-N SHOW DIFFERENT CYTOTOXIC EFFECTS
Zampagni
M*, Becatti M, Wright D, Campioni S, Mannini B, Cascella R, Chiti F, Stefani M,
Cecchi C
P49 - CELL DAMAGE INDUCED BY
EXPANDED ATAXIN-1 INVOLVES MECHANICAL INSTABILITY OF NUCLEAR MEMBRANE
Averaimo
S, Canale C, Pesci D, Fortunati V, Paulis D, Gliozzi A, Relini A, Mazzanti M,
Jodice C*
P50 - PORCINE NEURONAL MODELS
THAT RECAPITULATE HD PATHOGENESIS IN VITRO
Hruska-Plochan
M*, Vodicka P, Lackova M, Usvald D, Juhas S, Hrdlickova R, Miyanohara A,
Marsala M, Motlik J
P51 - NEW INSIGHTS INTO THE
FIBRILLOGENESIS PROCESS OF ATAXIN-3, A MODEL PROTEIN FOR STUDIES ON POLYQ
DISEASES
Invernizzi
G, Frana AM, Aprile FA, Natalello A, Relini A, Doglia SM, Tortora P, Regonesi
ME
P52 - ATAXIN-3 PROTEIN CONTEXT
AND CELL-SPECIFIC FACTORS MODULATE POLYQ-MEDIATED NEURONAL AGGREGATION IN A C
ELEGANS MODEL OF MACHADO-JOSEPH DISEASE
Andreia
Teixeira-Castro, Richard Morimoto, Patricia Maciel
P53 - EFFECT OF SOD1 EXPRESSION
IN A MUSCLE CELL MODEL OF FAMILIAL AMYOTROPHIC LATERAL SCLEROSIS
Onesto
E, Galbiati M, Zito A, Sau D, Crippa V, Poletti A
P54 - ROLE OF JNK IN EXCITOTOXIC
CELL DEATH FOLLOWING SEIZURE ACTIVITY
*G
Spigolon, C Veronesi, T Herdegen, C Bonny, A F Vercelli
P55 - VEGF PROTECTS MOTOR
NEURONS AGAINST EXCITOTOXICITY BY UPREGULATION OF GLUR2
Elke
Bogert*, Philip Van Damme, Koen Poesen, Joke Dhondt, Nicole Hersmus, Dora
Kiraly, Wendy Scheveneels, Wim Robberecht & Ludo Van Den Bosch
P56 - ROLE OF JNK IN EXCITOTOXIC
CELL DEATH FOLLOWING SEIZURE ACTIVITY
*G
Spigolon, C Veronesi, T Herdegen, Y Zhao, C Bonny, A E Vercelli
P57 - LOSS OF PARKIN PROTEIN
CAUSES ABNORMAL INTRACELLULAR CALCIUM LEVELS UPON GLUTAMATERGIC STIMULATION IN
NEURONAL CELLS
Sassone
J,Ascardi C,Zippel R,Colciago C, Tiloca C, Silani V, Ciammola A
P58 - RETINOIC ACID INHIBITS
P38-PHOSPHORYLATION AND PROTECTS AGAINST PREFIBRILLAR BETA-AMYLOID AND
GLUTAMATE TOXICITY
Zoia
CP*, Riva C, Proserpio P, Salerno D, Tremolizzo L, Ferrarese C
P59 - CEFTRIAXONE TREATMENT
IMPROVES PHENOTYPE IN A MURINE MODEL OF SPINAL MUSCULAR ATROPHY
D
Ronchi*, M Nizzardo, M Nardini, S Salani, C Simone, M Falcone, C Donadoni,
NBresolin, GP Comi, S Corti,
P60 - HIGH AFFINITY GLUTAMATE
TRANSPORTERS GLAST AND EAAC1 ARE PRESENT IN SCHWANN CELLS
Magnaghi
V, Di Cairano ES, Ballabio M, Perego C
P61 - MUSCLE-RESTRICTED
OVEREXPRESSION OF IGF-1 ATTENUATES DISEASE IN A MOUSE MODEL OF SPINAL AND
BULBAR MUSCULAR ATROPHY
Pennuto
M, Palazzolo I, Kong L, Sumner C, Hadachi H, Katsuno M, Sobue G, Taylor JP,
Fischbeck K
P62 - PROTEOMIC PROFILING OF
PRP27-30-ENRICHED PREPARATIONS EXTRACTED FROM THE BRAIN OF HAMSTERS WITH
EXPERIMENTAL SCRAPIE
Giorgi
A, Di Francesco L, Principe S, Mignogna G, Sennels L, Mancone C, Alonzi T,
Sbriccoli M, De Pascalis A, Rappsilber J, Cardone F, Pocchiari M, Maras M, Schinine
ME*
P63 - CHARACTERIZATION OF THE
MOLECULAR DIVERSITY OF PRION PROTEIN AGGREGATES
E
Biasini, L Tapella, R Chiesa
P64 - A NEW TRANSGENIC MOUSE
MODEL OF INHERITED PRION DISEASE
Dossena
S, Imeri L, Mangieri M, Garofoli A, Ferrari L, Senatore A, Restelli E, Balducci
C, Fiordaliso F, Salio M, Bianchi S, Fioriti L, Morbin M, Pincherle A, Marcon
G, Villani F, Carli M, Tagliavini F, Forloni G, Chiesa R
P65 - RRS1 IS INVOLVED IN
ENDOPLASMIC RETICULUM STRESS RESPONSE IN HUNTINGTON'S DISEASE
Carnemolla
A*, Fossale E*, Agostoni E, Michelazzi S, Calligaris R, De Maso L, Del Sal G,
MacDonald ME, Persichetti F
P66 -
MUTANT PRION PROTEIN EXPRESSION CAUSES IMPAIRMENT OF VOLTAGE-GATED CALCIUM
CHANNELS IN A TRANSGENIC MOUSE MODEL
Senatore
A, Colleoni S, Verderio C, Restelli E, Mantovani S, Condliffe S, Congi L,
Prestori F, Forloni G, DŐAngelo E, Matteoli M, Gobbi M, Chiesa R
Poster
Session I (P67-P133)
Sunday,
May 10, 2009
from 13:30
to 15:00
________________________________________________________________
P67 - MOLECULAR AND FUNCTIONAL
ANALYSIS OF PARAPLEGIN GENE (SPG7) MUTATIONS IN PATIENTS WITH FAMILIAL AND
SPORADIC SPASTIC PARAPLEGIA
D
DiBella*, M Plumari, S Magri, V Fracasso, F Lazzaro, M Muzi-Falconi, R
Fancellu, S DiDonato, D Pareyson, C Gellera, C Mariotti, S Baratta, F Taroni
P68 - EXPRESSION MODULATION OF A
SMALL HEAT SHOCK PROTEIN INVOLVED IN NEURODEGENERATIVE DISEASES
Crippa
V*, Boncoraglio A, Simonini F, Rusmini P, Poletti A
P69 - ROLE OF ALTERED
PROTEOLYSIS IN THE DEGENERATION OF MOTOR NEURONS IN IN VIVO MODELS OF FAMILIAL
AMYOTROPHIC LATERAL SCLEROSIS INVOLVEMENT OF CONSTITUTIVE AND IMMUNO
PROTEASOMES
Fontana
E*, Vitellaro-Zuccarello L, Cheroni C, Marino M, De Biasi S, Bendotti C
P70 - TDP-43 REDISTRIBUTION IS
AN EARLY EVENT IN SPORADIC AMYOTROPHIC LATERAL SCLEROSIS
Giordana
MT,Piccinini M,Grifoni S*, De Marco G, Vercellino M,Magistrello M, Pellerino A,
Buccinn B, Lupino E, Rinaudo MT
P71 - AUTOPHAGIC CLEARANCE OF
THE PARKINSON'S DISEASE-ASSOCIATED GPR37 RECEPTOR
Di
Pietro C, Marazziti D, Golini E, Mandillo S, Matteoni R, Tocchini-Valentini GP
P72 - GEC1 : A NEW AUTOPHAGY
EFFECTOR HIGHLY EXPRESSED IN THE SNC
Chakrama
FZ*, Seguin S, Fraichard A, Delage-Mourroux R, Jouvenot M, Boyer-Guittaut M
P73 - GREY-LETHAL MOUSE: A
MURINE MODEL FOR MALIGNANT OSTEOPETROSIS AND A NEW NEURONAL LYSOSOMAL STORAGE
DISEASE
Frattini
A, De Biasi S, Strina D, Vitellaro Zuccarello L, Fontana E, Gioria M, Valnegri
P, Sala C, Costantino-Ceccarini E
P74 - BRAIN NEURODEGENERATION
AND INTERFERON GENE EXPRESSION ANALYSIS IN THE CEREBRO-SPINAL FLUID OF
AICARDI-GOUTIRES PATIENTS
Izzotti
A, Cartiglia C, Longobardi M, Pulliero A
P75 - TRANSCRIPTIONAL SIGNATURES
IN NEURODEGENERATIVE DISEASES
Daniela
Diamanti*, Pollio Giuseppe, Tarditi Alessia, Remelli Rosaria, Caricasole Andrea
P76 - THE EXPRESSION OF THE
STEROIDOGENIC ACUTE REGULATORY PROTEIN (STAR) IS INCREASED IN THE DEGENERATING
TRAIT OF SPINAL CORD OF WOBBLER MICE
Tartari
S*, Bigini P, Orly J, Mennini T, Cantoni L
P77 - REST, THE TRANSCRIPTION
REPRESSOR THAT GOVERNS NEUROSECRETION EXPRESSION, APPEARS TO HAVE A ROLE ALSO
IN THE EXPRESSION OF GLIOSECRETION
Prada
I*, DŐAlessandro R, Stucchi L, Meldolesi J
P78 - PARK2 PATIENT FIBROBLASTS
TRANSCRIPTOME ANALYSES INDICATE A ROLE OF PARKIN IN ENDOCYTOSIS
Klinkenberg
M*, Gispert S, Morales-Gordo B, Walter M, Auburger G
P79 - AMYOTROPHIC LATERAL
SCLEROSIS: A HIGH THROUGHPUT ANALYSIS USING PHARMACOLOGICAL AND GENETICALLY
MODIFIED CELLULAR MODELS
Lenzken
SC*, Della Beffa C, Bonanno D, Zolezzi F, Vivarelli S, Carri' MT, Calogero R,
Barabino SML
P80 - TNF-ALPHA mRNA AND PROTEIN
EXPRESSION IN SPORADIC ALS PATIENTS
Guareschi
S, Cova E, Baiocchi C, Milani O, Federici Canova D, Cuccia M, Ceroni M, Cereda
C*
P81 - REGULATION OF MRNA
STABILITY BY THE RNA BINDING PROTEIN TNRC4 IN NEURONAL DIFFERENTIATION
Viero
G*, Vessey J, Savino M, DŐApolito M, Grifa A, Macchi P ,Quattrone A
P82 - TRANSCRIPTIONAL REGULATION
OF GLYCOSPHINGOLIPIDS DEGRADING ENZYMES
Urbanelli
L, Trivelli F, Magini A, Tancini B, Ciccarone V, Polidoro M, Emiliani C*
P83 - PATHOGENETIC MECHANISMS IN
THE CONGENITAL CENTRAL HYPOVENTILATION SYNDROME (CCHS)
Benfante
R*, Di Lascio S, Bachetti T, Ceccherini I, Fornasari D
P84 - TRANSCRIPTIONAL CHANGES IN
A CELLULAR MODEL OF HUNTINGTONŐS DISEASE
Rosenstock
TR*, Oliveira CR, Rego AC
P85 - MICROARRAY ANALYSIS
UNVEILS THE INVOLVEMENT OF ADDITIONAL PATHWAYS IN DJ-1 MEDIATED
NEURODEGENERATION
Foti
R, Zucchelli S, Biagioli M, Roncaglia P, Pinto M, Carrieri C, Vilotti S, Krmac
H, Calligaris R, Gustincich S
P86 - GENE DYSREGULATION IN
FRAGILE X-ASSOCIATED TREMOR/ATAXIA SYNDROME
F
Tassone F, Garcia-Arocena D, Iwahashi C, Greco C, Hagerman RJ, PJ Hagerman PJ
P87 - STUDIES ON THE
PATHOPHYSIOLOGY OF NEUROLOGICAL INVOLVEMENT IN A MUCOPOLYSACCHARIDOSIS TYPE I
MOUSE MODEL
Marika
Salvalaio, Rosella Tomanin, Elisa Legnini, Francesca DŐAvanzo, Antonello
DŐArrigo, Alberta Leon, Maurizio Scarpa
P88 - OXIDATIVE AND ANTIOXIDANT
MARKERS IN PATIENTS WITH NEURODEGENERATIVE DISEASES: A PILOT STUDY TO ESTIMATE
RISK AND PROTECTIVE FACTORS
Gironi
Russo Bianchi Angelini Martinelli-Boneschi Cursano MarianiBonalumi
KulmannCeresa Farina, Alberoni Nemni
P89 - EFFECTS OF BEE VENOM ON
SYMPTOMATIC AMYOTROPHIC LATERAL SCLEROSIS MODEL
Eun
Jin Yang, Jing Hua Jiang, Hye Suk Hwang, Myeong Soo Lee, Sun Mi Choi
P90 - POSTTRAUMATIC
GABA(A)-MEDIATED [Ca2+]I INCREASE IS ESSENTIAL FOR THE INDUCTION OF
BDNF-DEPENDENT SURVIVAL OF MATURE CENTRAL NEURONS
Shulga
A*, Thomas-Crusells J, Sigl T, Blaesse A, Mestres P, Meyer M, Yan Q, Kaila K,
Saarma M, Rivera C, Giehl KM
P91 - ACETYLCHOLINE INDUCES
CHANGES IN PROTEIN FOLDING REGIMEN AND CYTOSKELETON ORGANIZATION
Lombardi
B, Giorgi A, Mignogna G, Orlando V, Biagioni S, Augusti-Tocco G, Schinine ME*
P92 - CHRONIC TREATMENT WITH
AMYLOID beta1-42 CHANGES AGONIST BINDING AT M1 AND M3 MUSCARINIC RECEPTORS
EXPRESSED IN cho CELLS
Smyckova
H, Jakubik J, Dolezal V
P93 - THE GTPase AND THE KINASE
DOMAINS OF THE PARKINSON'S DISEASE ASSOCIATED LRRK2: A CLOSE RELATIONSHIP
Greggio
E, Taymans J-M, Beilina A, Vancraenenbroeck R, Baekelandt V, Cookson MR
P94 - ROLE OF ATAXIN-3 PHOSPHORYLATION
IN SPINOCEREBELLAR ATAXIA TYPE 3 (SCA3) PATHOGENESIS
Pastori
V, Sangalli E, Nonnis S, Tedeschi G, Coccetti P, Fusi P
P95 - ANTIBODIES AGAINST
NEURONAL NICOTINIC ACETYLCHOLINE RECEPTORS: POTENTIAL ROLE IN NEURODEGENERATION
Lykhmus
OYu, Koval LM, Gergalova GL, Cloez-Tayarani I, Tzartos SJ, Tsetlin VI,
Bachinskaya NYu, Skok MV*
P96 - GENETIC REPROGRAMMING OF
DISEASE-SPECIFIC FIBROBLASTS
Ungaro
F, Loponte S, Laterza C, Di Stefano B and Broccoli V
P97 - FUNCTIONAL CONSEQUENCES OF
WASH-RESISTANT XANOMELINE BINDING AT M2 AND M4 MUSCARINIC RECEPTORS
Machova
E, Jakubik J, El-Fakahany EE, Dolezal V
P98 - INFLUENCE OF ALCURONIUM ON
ACTIVATION OF M1-M4 MUSCARINIC RECEPTORS SIGNALLING BY CARBACHOL
Randakova
A, Jakubik J, El-Fakahany EE, Dolezal V
P99 - MATHEMATICAL MODELING AND
SIMULATION OF NEURO-CHIPS
Sacco
R
P100 - INFLUENCE OF MEMBRANE
CHOLESTEROL CONTENT ON MUSCARINIC RECEPTOR STIMULATION OF GQ/11 G-PROTEIN
SIGNALING
Michal
P, Rudajev V, El-Fakahany EE, Dolezal V
P101 - CEREBELLAR IMMUNOLOCALIZATION
OF THE GUANINE EXCHANGE FACTOR RASGRF1 AND CHANGES IN THE PROTEOME PROFILE
INDUCED BY ITS GENETIC DELETION IN MICE
Rusconi
F*, Colombo G, Fontana E, Bachi A, Vitellaro-Zuccarello L, Zippel R, De Biasi S
P102 -
17-(ALLYLAMINO)-17-DEMETHOXYGELDANAMYCIN (17-AAG) A PHARMACOLOGICAL APPROACH TO
INDUCE DEGRADATION OF MISFOLDED PROTEINS
Rusmini
P, Crippa V, Simonini F, Bolzoni E, Poletti A
P103 - MOLECULAR BIOMARKER/S OF
HUNTINGTON'S DISEASE PATHOGENESIS IN HUMAN PERIPHERAL BLOOD AND CLONALLY STRIATA-DERIVED
RAT CELLS
Bregant
E, Temil L, Marcuzzi F, Passon N,Siciliano G, Ceravolo R,Unti E, Damante G, and
IR Lonigro*
P104 - THE ROLE OF REST AND ITS
ASSOCIATED COFACTOR BHC80 IN MODULATING NEURONAL FUNCTIONS
Klajn
A, Ferrai C, Stucchi L, Prada I, Meldolesi J, DŐAlessandro R*
P105 - WALLERIAN-LIKE DISTAL
AXONAL DEGENERATION FOLLOWING LOCAL AXOTOMY IN A NOVEL MICROFLUIDIC CULTURE
SYSTEM
Kilinc
D*, Peyrin JM, Saias L, Soubeyre V, Viovy JL, and Brugg B
P106 - SOD1 EFFECT ON CELL CYCLE
PROGRESSION IN AN ALS MODEL
Ghiroldi
A, Bianchi M, Mazzini G, Guareschi S, Ceroni M, Cereda C*, Cova E
P107 - TEMPORAL EVOLUTION OF
SPINAL NETWORK ACTIVITY IN WILD TYPE AND G93A MUTANT MOUSE ORGANOTYPIC CULTURES
Rancic
V, Villari A, Ballerini L
P108 - PROTEINS RELATED TO
NEURODEGENERATION ARE DIFFERENTIALLY EXPRESSED IN FIBROBLASTS FROM FAMILIAL
ALZHEIMER'S DISEASE MUTATION CARRIERS, BOTH SYMPTOMATIC AND PRE-SYMPTOMATIC
Magini
A, Ciccarone V, Tancini B, Urbanelli L, Trivelli F, Polidoro M, Sorbi S, Zolla
L, Emiliani C*
P109 - 9,10-ANTHRAQUINONE
INTERFERES WITH Abeta-PEPTIDE AGGREGATION: MECHANISM OF ACTION
Convertino
M*, Pellarin R, Catto M, Carotti A, Caflisch A
P110 - ALTERED AXONAL GROWTH OF
CULTURED SYMPATHETIC NEURONS FROM DYSTROPHIC MDX MICE
Lombardi
L*, De Stefano ME, Hoogenraad CC, Paggi P
P111 - ECTOPIC ATP SYNTHESIS: A
NEW CORRELATION BETWEEN MITOCHONDRIAL DISORDERS AND NEURODEGENERATIVE DISEASES
Ravera
S, Calzia D, Bianchini P, Aluigi MG, Diaspro A, Mancardi G, Morelli A, Pepe IM,
Panfoli I*
P112 - EFFECT OF GABA-A RECEPTOR
SIGNALLING MODULATION ON NEURAL PRECURSORS
Fila
T, Ciccolini F
P113 - PHENOTYPICAL
CHARACTERIZATION OF THIRD TRIMESTER HUMAN AMNIOTIC FLUID CELLS WITH POTENTIAL
FOR THERAPY IN NEURODEGENERATIVE DISORDERS
Cigognini
D*, Nicora E, Ripamonti E, Adami R, Abrignani S, Moro M, Rebulla P, Di Giulio
AM, Bottai D, Gorio A
P114 - MOTONEURON
TRANSPLANTATION RESCUE THE PHENOTYPE OF SPINAL MUSCULAR ATROPHY WITH
RESPIRATORY DISTRESS TYPE 1 (SMARD1)
Monica
Nizzardo*, Stefania Corti, Martina Nardini, Chiara Donadoni, Sabrina Salani,
Dario Ronchi, Roberto Del Bo, Dimitra Papadimitriou, Federica Locatelli, Nereo
Bresolin, Giacomo P Comi,
P115 - NEURAL STEM CELLS DERIVED
FROM GENETICALLY ENGINEERED, LINEAGE-SELECTABLE ES CELLS IMPROVES THE PHENOTYPE
OF A MOUSE MODEL OF SPINAL MUSCULAR ATROPHY
C
Simone*, S Corti, M Nizzardo, S Salani, M Nardini, C Donadoni, D Ronchi, M
Falcone, N Bresolin, GP Comi,
P116 - MATRIX
METALLOPROTEINASE-9 INCREASES IN THE STRIATUM AND SUBSTANTIA NIGRA OF A MOUSE
MODEL OF PARKINSONISM: AN mRNA EXPRESSION, PROTEIN LEVEL AND IMMUNOLOCALIZATION
STUDY
Annese
V, Barcia C, Ros Bernal F, Paggi P, Herrero MT and De Stefano ME*
P117 - AN IN VITRO MODEL OF GLIA
ACTIVATION TO DISSECT THE SPECIFIC ROLES OF ASTROCYTES AND MICROGLIA IN
NEURODEGENERATIVE DISEASES
Consonni
A, Macco R, Pelizzoni I, Bettegazzi B, Vitali I, Morini M, Rossi FM, Codazzi F,
Grohovaz F, Zacchetti D
P118 - NERVE GROWTH FACTOR (NGF)
RESTORES NEURONAL AND GLIAL FUNCTION IN THE SPARED NERVE INJURY (SNI) MODEL OF
NEUROPATHIC PAIN
Cirillo
G, Bianco MR, Colangelo AM*, Cavaliere C, De Luca D, Viggiani S, Fragni M,
Alberghina L, Papa M
P119 - IS MICROTUBULE DYNAMICS
IMBALANCE AN EARLY EVENT IN MPTP-INDUCED NEUROGENERATION?
Cartelli
D*, Molinaro G, Busceti CL, Battaglia G, Giavini E, and Cappelletti G
P120 - THE MODULATION OF
D-SERINE CONCENTRATION IN THE BRAIN AS A MOLECULAR MECHANISM IN SCHIZOPHRENIA
SUSCEPTIBILITY
Sacchi
S*, Cappelletti P, Caldinelli L, Martineau M, Mothet JP, Molla G, Pollegioni L
P121 - NEUROMYELITIS OPTICA
AUTOANTIBODIES SELECTIVELY RECOGNIZE AQUAPORIN-4 ORTHOGONAL ARRAYS OF PARTICLES
Pisani
F*, Nicchia GP, Mastrototaro M, Rossi A, Tortorella C, Ruggieri M, Lia A,
Trojano M, Frigeri A, Svelto M
P122 - SOLIDITY OF THE REDUCTION
OF THE CHOLESTEROL BIOSYNTHESIS PATHWAY IN HD AND POTENTIAL REGULATORY ROLE OF
NORMAL HUNTINGTIN
Petricca
L*, Valenza M, Leoni V, Pouladi MA, Carroll J, Fossale E, Nguyen HP, Riess O,
MacDonald M, Hayden M, DiDonato S, Cattaneo E
P123 - ROLE OF IGF-1 AUTOCRINE
SECRETION AND SIRTUINS REDISTRIBUTION IN THE RESISTANCE OF NEURONAL
DIFFERENTIATED CELLS TO STS-INDUCED CELL DEATH
Tafani
M*, Indelicato M, Aventaggiato M, Reali V, Marfe G, Rosa R, Pucci B, Russo MA
P124 - FETAL-DERIVED NEURAL STEM
(NS) CELLS RETAIN THE IN VIVO POSITIONAL INFORMATION CODE AND DIFFERENTIATE IN
APPROPRIATE NEURONAL LINEAGES
Onorati
M*, Conti L, Binetti M, Camnasio S, Calabrese G, Consalez GG, Cattaneo E
P125 - A NEW SYSTEMATIC APPROACH
TO DETECT BDNF MRNA IN HUMAN BLOOD SAMPLES
Marullo
M, Zuccato C, Di Donato S, Mariotti C, Vandesompele J, Cattaneo E
P126 - AN EVOLUTIONARY APPROACH
TO THE STUDY OF HUNTINGTIN, THE PROTEIN CAUSING HUNTINGTON'S DISEASE
Lo
Sardo Valentina, Zuccato Chiara, Ramos Catarina, Tartari Marzia, Cattaneo Elena
P127 - ASTROCYTES DERIVED FROM
NEURAL PRECURSOR CELLS OF WOBBLER MICE INDUCE APOPTOTIC DEATH OF MOTOR NEURONS
THROUGH REDUCED GLUTAMATE TRANSPORT
Diana
V, Ottolina A, Botti F, Fumagalli E, Calcagno E, De Paola M, Cagnotto A,
Invernici G, Parati E, Curti D, Mennini T
P128 - GENERATION OF iPS CELLS
FOR MECHANISTICS STUDIES IN HUNTINGTON'S DISEASE
Christelle
Rochon*, Valentina Castiglioni, Alessia Delli Carri, Luciano Conti, Caterina
Mariotti, Stefano DiDonato, Marisa Jaconi, Outi Hovatta, Anis Feki, Elena
Cattaneo
P129 - THE DIVERSITY OF LIFE: AN
APPROACH
Garzn
L, Cavero A
P130 - GENETIC
INTERACTION BETWEEN THE m-AAA PROTEASE ISOENZYME REVEALS NOVEL ROLES IN
NEURODEGENERATION
Martinelli
P*, La Mattina V, Bernacchia A, Magnoni R, Cerri F, Cox G, Casari G, Quattrini A,
Rugarli EI
P131 - SPASTIN:A
BRIDGE BETWEEN CYTOSKELETAL REMODELING AND MEMBRANE TRAFFICKING VIA
PROTRUDIN-RAB11 PATHWAY
Martignoni
M, Rugarli EI
P132 - ROLE
OF THE AXONAL-SMN (a-SMN) PROTEIN IN AXON GROWTH AND SPINAL MUSCULAR ATROPHY
(SMA) PATHOGENESIS
Locatelli
D*, D'Errico P, Terao M, Capra S, Regano D, Garattini E, Battaglia G.
P133 -
SELADIN-1 AND BETA-AMYLOID TOXICITY ARE MODULATED BY GnRH.
Zito
A, Cariboni A, Piva F, Maggi R, Galbiati M